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| 1 | Hyperammonemia crisis following parturition in a female patient with ornithine transcarbamylase deficiency显示文摘Ornithine transcarbamylase deficiency(OTCD) is an X-linked disorder,with an estimated prevalence of 1 per 80000 live births.Female patients with OTCD develop metabolic crises that are easily provoked by non-predictable common disorders,such as genetic(private mutations and lyonization) and external factors;however,the outcomes of these conditions may differ.We resuscitated a female patient with OTCD from hyperammonemic crisis after she gave birth.Hyperammonemia after parturition in a female patient with OTCD can be fatal,and this type of hyperammonemia persists for an extended period of time.Here,we describe the cause and treatment of hyperammonemia in a female patient with OTCD after parturition.Once hyperammonemia crisis occurs after giving birth,it is difficult to improve the metabolic state.Therefore,it is important to perform an early intervention before hyperammonemia occurs in patients with OTCD or in carriers after parturition. | Jun Kido Tatsuya Kawasaki Hiroshi Mitsubuchi Hidenobu Kamohara Takashi Ohba Shirou Matsumoto Fumio Endo Kimitoshi Nakamura | 2017 | World Journal of Hepatology2017，9，6： | 3 |
| 2 | Wilson disease developing osteoarthritic pain in severe acute liver failure: A case report显示文摘BACKGROUND Wilson disease (WD) is a rare copper metabolism disorder with symptoms including hepatic disorders, neuropsychiatric abnormalities, Kayser-Fleischer rings, and hemolysis in association with acute liver failure (ALF). Osteoarthritis is a rare manifestation of WD. We experienced a case of WD with arthritic pain in the knee and liver cirrhosis. Here, we report the clinical course in a WD patient with arthritic pain and liver cirrhosis receiving combination therapy with Zn and a chelator and discuss the cause of arthritic pain. CASE SUMMARY We present an 11-year-old boy who developed osteoarthritis symptoms and ALF, with a New Wilson Index Score (NWIS) of 12. He was diagnosed with WD with decreased serum ceruloplasmin and copper levels, increased urinary copper excretion, and ATP7B gene mutations detected on gene analysis. There was improvement in the liver cirrhosis, leading to almost normal liver function and liver imaging, one year after receiving combination therapy with Zn and a chelator. Moreover, his arthritic pain transiently deteriorated but eventually improved with a decrease in the blood alkaline phosphatase levels following treatment. CONCLUSION Patients with WD who develop ALF with an NWIS > 11 may survive after treatment with Zn and chelators, without liver transplantation, when they present with mild hyperbilirubinemia and stage ≤ II hepatic encephalopathy. Osteoarthritis symptoms may improve with long-term Zn and chelator therapy without correlation of liver function in WD. | Jun Kido Shirou Matsumoto Keishin Sugawara Kimitoshi Nakamura | 2019 | World Journal of Hepatology2019，11，7： | 2 |
| 3 | Successful treatment of giant rectal varices by modified percutaneous transhepatic obliteration with sclerosant:Report of a case显示文摘We present a female patient with continuous melena, diagnosed with rectal variceal bleeding. She had a history of esophageal varices, which were treated with endoscopic therapy. Five years after the treatment of esophageal varices, continuous melena occurred. Since colonoscopy showed that the melena was caused by giant rectal varices, we thought that they were not suitable to receive endoscopic treatment. We chose the modified percutaneous transhepatic obliteration with sclerosant, which is one of the interventional radiology techniques but a new clinical procedure for rectal varices. After the patient received this therapy, her condition of rectal varices was markedly improved. | Hirotoshi Okazaki Kazuhide Higuchi Masatsugu Shiba Shirou Nakamura Tomoko Wada Kazuki Yamamori Ai Machida Kaori Kadouchi Akihiro Tamori Kazunari Tominaga Toshio Watanabe Yasuhiro Fujiwara Kenji Nakamura Tetsuo Arakawa | 2006 | World Journal of Gastroenterology2006，12，33： | 2 |
| 4 | Method for the proposal and evaluation of urban structures for compact cities using an expert system显示文摘 | Shirou Tsuboi Shinji Ikaruga Takeshi Kobayashi | 2016 | Frontiers of Architectural Research2016，5，4： | 2 |
| 5 | Small bowel anisakiosis: A report of two cases显示文摘小肠狭窄是肠的 anisakiosis 的严肃的复杂并发症。这份报告的目的是调查小肠的严重狭窄是否能保存地被管理。我们与 anisakiosis 引起的小肠的严重狭窄对待二个病人。外科的干预最后被执行在上第 23 和第 35 在医院里分别地。 resected 标本的组织病理学说的检查表明肠的墙被 anisakiosis 的炎性反应完全损坏了,并且损坏是不可逆的,从而建议那剖腹术在严重的小肠狭窄的情况下被需要由肠的 anisakiosis 引起了,就算为肠的 anisakiosis 的保守疗法的一个长时期允许病人通过尖锐阶段成功地过去。 | Shigetoshi Matsuo Takashi Azuma Seiya Susumu Satoshi Yamaguchi Shirou Obata Tomayoshi Hayashi | 2006 | World Journal of Gastroenterology2006，12，25： | 1 |
| 6 | Responses of human glioblastoma cells to human natural tumor necrosis factor-α: Susceptibility, mechanism of resistance and cytokine production studies显示文摘 | Shirou Sakuma Yutaka Sawamura Mitsuhiro Tada Toshimitsu Aida Hiroshi Abe Keiichiro Suzuki Naoyuki Taniguchi | 1993 | Journal of Neuro - Oncology1993，，3： | 1 |
| 7 | Coupled Lateral-Torsional Vibration of Rotor System Train by Gears显示文摘 | Takuzo T Shirou A | 1984 | Bulletin of JSME1984，27，224： | 1 |
| 8 | Age form- ing technology for aircraft wing skin显示文摘 | TAKAFUMI A SHIROU K TAKAHIRO N | 2004 | Materials Forum2004，28，： | 1 |
| 9 | Evaluation of renal arteries in living renal donors: comparison between MDCT angiography and gadolinium-enhanced 3D MR angiography显示文摘 | Tonsok Kim Takamichi Murakami Satoru Takahashi Masatoshi Hori Shirou Takahara Naotsugu Ichimaru Akihiko Okuyama Yoshifumi Narumi Hironobu Nakamura | 2006 | Radiation Medicine2006，，9： | 1 |
| 10 | Whole-Body Gallium-67 Scintigraphic Findings in IgG4-Related Disease显示文摘 | Shirou Ishii Fumio Shishido Masayuki Miyajima Koutarou Sakuma Takeshi Shigihara Ken Kikuchi | 2011 | Clinical Nuclear Medicine2011，，7： | 1 |
| 11 | Comparison of Alzheimer’s disease with vascular dementia and non-dementia using specific voxel-based Z score maps显示文摘 | Shirou Ishii Fumio Shishido Masayuki Miyajima Koutarou Sakuma Takeshi Shigihara Tadanobu Tameta Makoto Miyazaki Hiroshi Kuroda | 2009 | Annals of Nuclear Medicine2009，，1： | 1 |
| 12 | Suppression of arterial intimal hyperplasia by cilostamide, a cyclic nucleotide phosphodiesterase 3 inhibitor,in a rat balloon double-injury model 显示文摘 | Kazuyuki T Toshikisudo Kaxue T Shirou T Yukio K | 2000 | Br J Pharmacol2000，130，： | 1 |
| 13 | In vitro and in vivo antioxidant properties of chlorogenic acid and caffeic acid显示文摘 | Yuki Sato Shirou Itagaki Toshimitsu Kurokawa Jiro Ogura Masaki Kobayashi Takeshi Hirano Mitsuru Sugawara Ken Iseki | 2010 | International Journal of Pharmaceutics2010，，： | 1 |
| 14 | Artificial neural network modeling to predict the plasma concentration of aminoglycosides in burn patients显示文摘 | Shigeo Yamamura Keiko Kawada Rieko Takehira Kenji Nishizawa Shirou Katayama Masaaki Hirano Yasunori Momose | 2004 | Biomedicine & Pharmacotherapy2004，，4： | 1 |
| 15 | Mutations in the hepatocyte nuclear factor-1α gene (MODY3) are not a major cause of early-onset non-insulin-dependent (type 2) diabetes mellitus in Japanese显示文摘 | Hidekazu Nishigori Shirou Yamada Tomoko Kohama Toshihiro Utsugi Hiroyuki Shimizu Toshiyuki Takeuchi J. Takeda | 1998 | Journal of Human Genetics1998，，2： | 1 |
| 16 | Protective effect of lutein after ischemia-reperfusion in the small intestine显示文摘 | Yuki Sato Masaki Kobayashi Shirou Itagaki Takeshi Hirano Toshihiro Noda Satoshi Mizuno Mitsuru Sugawara Ken Iseki | 2011 | Food Chemistry2011，，3： | 1 |
| 17 | Improvement of the Tissue-adhesive and Sealing Effect of Fibrin Sealant Using Polyglycolic Acid Felt显示文摘 | Noriko Shinya Shirou Oka Sumika Miyabashira Hiroshi Kaetsu Takanori Uchida Masuo Sueyoshi Kozo Takase Masao Akuzawa Atsushi Miyamoto Takamichi Shigaki | 2009 | Investigative Surgery2009，，5： | 1 |
| 18 | Outcomes of Extended Radical Esophagectomy for Thoracic Esophageal Cancer显示文摘 | Tadashi Nishimaki Tsutomu Suzuki Satoshi Suzuki Shirou Kuwabara Katsuyoshi Hatakeyama | 1998 | Journal of the American College of Surgeons1998，，3： | 1 |
| 19 | Neoadjuvant intraarterial chemotherapy for stage IIB-IIIB cervical cancerin Japanese women显示文摘 | Shoji Kaku Kentaro Takahashi Yoshitaka Murakami Shirou Wakinoue Tetsuya Nakagawa Yoshihiko Shimizu Nobuyuki Kita Yoichi Noda Takashi Murakami | 2010 | Experimental and Therapeutic Medicine2010，，4： | 1 |
| 20 | Surgical approach to tumor recurrence and metastatic lesions of the liver in a patient with malignant endocrine tumors of the pancreas: case report显示文摘 | Mitsuhiro Inagaki Takeshi Aoyagi Atsushi Nomura Hideki Yokoo Mitsuhiro Akabane Akira Kawata Shirou Nakano Atsushi Chiba Tsuneshi Fujii Hiroharu Sakurai Toshihiko Tsukada Masahiro Takahashi | 2003 | Journal of Hepato-Biliary-Pancreatic Surgery2003，，4： | 1 |
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