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| 1 | Management of cholelithiasis in Italian children:A national multicenter study显示文摘AIM:To evaluate the management of Italian children with cholelithiasis observed at Pediatric and Surgical Departments linked to Italian Society of Pediatric Gastroenterology Hepatology and Nutrition. METHODS: One-hundred-eighty children (90 males, median age at diagnosis 7.3 years; range, 0-18 years) with echographic evidence of cholelithiasis were enrolled in the study; the data were collected by an anonymous questionnaire sent to participating centers. RESULTS: One hundred seventeen patients were treated with ursodeoxycholic acid; in 8 children dissolution of gallstones was observed, but the cholelithiasis recurred in 3 of them. Sixty-five percent of symptomatic children treated became asymptomatic. Sixty-four patients were treated with cholecystectomy and in only 2 cases a postoperative complication was reported. Thirty- four children received no treatment and were followed with clinical and echographic controls; in no case thedevelopment of complications was reported. CONCLUSION: The therapeutic strategies were extremely heterogeneous. Ursodeoxycholic acid was ineffective in dissolution of gallstones but it had a positive effect on the symptoms. Laparoscopic cholecystectomy was confirmed to be an efficacy and safe treatment for pediatric gallstones. | Claudia Della Corte Diego Falchetti Gabriella Nebbia Marisa Calacoci Maria Pastore Ruggiero Francavilla Matilde Marcellini Pietro Vajro Raffaele Iorio | 2008 | World Journal of Gastroenterology2008，14，9： | 6 |
| 2 | Evaluation of Pesticide Residues in Mango by a Multi-residue Analysis and GC/MS Triple Quadrupole显示文摘 | Claudia Helena Pastor Ciscato Kumi Shiota Ozawa Claudia Maria Barbosa Amir Bertoni Gebara | 2015 | Journal of Agricultural Science and Technology(B)2015，5，8： | 2 |
| 3 | Neither hereditary periodic fever nor periodic fever, aphthae, pharingitis, adenitis: Undifferentiated periodic fever in a tertiary pediatric center显示文摘AIM To describe the frequency and clinical characteristics of patients with undifferentiated periodic fever(UPF) and to investigate whether a clinical classification of UPF based on the PRINTO-Eurofever score can help predicting the response to treatment and the outcome at follow-up.METHODS Clinical and therapeutic information of patients with recurrent fever who presented at a single pediatric rheumatology center from January 2006 through April 2016 were retrospectively collected. Patients with a clinical suspicion of hereditary periodic fever(HPF) syndrome and patients with clinical picture of periodic fever, aphthae, pharingitis, adenitis(PFAPA) who were refractory to tonsillectomy underwent molecular analysis of five HPF-related genes: MEFV(NM_000243.2), MVK(NM_000431.3), TNFRSF1 A(NM_001065.3), NLRP3(NM_001079821.2), NLRP12(NM_001277126.1). All patients who had a negative genetic result were defined as UPF and further investigated. PRINTO-Eurofever score for clinical diagnosis of HPF was calculated in all cases. RESULTS Of the 221 patients evaluated for periodic fever, twelve subjects with a clinical picture of PFAPA who were refractory to tonsillectomy and 22 subjects with a clinical suspicion of HPF underwent genetic analysis. Twenty-three patients(10.4%) resulted negative and were classified as UPF. The median age at presentation of patients with UPF was 9.5 mo(IQR 4-24). Patients with UPF had a higher frequency of aphthae(52.2% vs 0%, P = 0.0026) and musculoskeletal pain(65.2% vs 18.2%, P = 0.0255) than patients with genetic confirmed HPF. Also, patients with UPF had a higher frequency of aphthous stomatitis(52.2% vs 10.7%, P < 0.0001), musculoskeletal pain(65.2% vs 8,0%, P < 0.0001), and abdominal pain(52.2% vs 4.8%, P < 0.0001) and a lower frequency of pharyngitis(56.6% vs 81.3%, P = 0.0127) compared with typical PFAPA in the same cohort. Twenty-one of 23 patients with UPF(91.3%) received steroids, being effective in 16; 13(56.2%) were given colchicine, which was effective in 6. Symptoms resolution occurred in 2 patients with UPF at last follow-up. Classification according to the PRINTOEurofever score did not correlate with treatment response and prognosis. CONCLUSION UPF is not a rare diagnosis among patients with periodic fever. Clinical presentation place UPF half way on a clinical spectrum between PFAPA and HPF. The PRINTOEurofever score is not useful to predict clinical outcome and treatment response in these patients. | Silvia De Pauli Sara Lega Serena Pastore Domenico Leonardo Grasso Anna Monica Rosaria Bianco Giovanni Maria Severini Alberto Tommasini Andrea Taddio | 2018 | World Journal of Clinical Pediatrics2018，7，1： | 2 |
| 4 | Evaluation of an aroma similar to that of sparkling wine:Sensory and gas chromatography analyses of fermented grape musts显示文摘 | Maria E O Mamede Helena M A B Cardello Glaucia M Pastore | 2005 | Food Chemistry2005，89，： | 1 |
| 5 | Enzymatic synthesis of short chain citronellyl esters by a new lipase from Rhizopus sp显示文摘 | Gabriela Alves Macedo Maria Mercedez Soberón Lozano Gláucia Maria Pastore | 2003 | Electronic Journal of Biotechnology2003，，6： | 1 |
| 6 | Intraduodenal Lipase Activity in Celiac Disease Assessed by Means of 13C Mixed-Triglyceride Breath Test显示文摘 | Francesco Perri Maria Pastore Virginia Festa Rocco Clemente Michele Quitadamo Mario R. D’Altilia Grazia Niro Paolo Paolucci Angelo Andriulli | 1998 | Journal of Pediatric Gastroenterology & Nutrition1998，，4： | 1 |
| 7 | Xylo-oligosaccharides from lignocellulosic materials: Chemical structure, health benefits and production by chemical and enzymatic hydrolysis显示文摘 | Ana Flávia Azevedo Carvalho Pedro de Oliva Neto Douglas Fernandes da Silva Gláucia Maria Pastore | 2013 | Food Research International2013，，1： | 1 |
| 8 | An update in neoadjuvant chemotherapy in cervical cancer显示文摘 | Pieluigi Benedetti Panici Filippo Bellati Maria Pastore Natalina Manci Angela Musella Simona Pauselli Michela Angelucci Ludovico Muzii Roberto Angioli | 2007 | Gynecologic Oncology2007，，1： | 1 |
| 9 | Production and properties of a surfactant obtained from Bacillus subtilis grown on cassava wastewater显示文摘 | Marcia Nitschke Glaucia Maria Pastore | 2006 | Bioresource technology2006，97，： | 1 |
| 10 | Volatile constituents of exotic fruits from Brazil显示文摘 | Juliano Lemos Bicas Gustavo Molina Ana Paula Dionísio Francisco Fábio Cavalcante Barros Roger Wagner Mário Roberto Maróstica Gláucia Maria Pastore | 2011 | Food Research International2011，，7： | 1 |
| 11 | Gene transfer of master autophagy regulator TFEB results in clearance of toxic protein and correction of hepatic disease in alpha‐1‐anti‐trypsin deficiency显示文摘 | Nunzia Pastore Keith Blomenkamp Fabio Annunziata Pasquale Piccolo Pratibha Mithbaokar Rosa Maria Sepe Francesco Vetrini Donna Palmer Philip Ng Elena Polishchuk Simona Iacobacci Roman Polishchuk Jeffrey Teckman Andrea Ballabio Nicola Brunetti‐Pierri | 2013 | EMBO Mol Med2013，，3： | 1 |
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