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30篇 您的检索式:作者名="Engelmann G"
    题名 作者 年代 出处 被引量
1Differential diagnosis in patients with suspected bile acid synthesis defects显示文摘AIM: To investigate the clinical presentations associated with bile acid synthesis defects and to describe identification of individual disorders and diagnostic pitfalls. METHODS: We describe semiquantitative determination of 16 urinary bile acid metabolites by electrospray ionization-tandem mass spectrometry. Sample preparation was performed by solid-phase extraction. The total analysis time was 2 min per sample. We determined bile acid metabolites in 363 patients with suspected defects in bile acid metabolism. RESULTS: Abnormal bile acid metabolites were found in 36 patients. Two patients had bile acid synthesis defects but presented with atypical presentations. In 2 other patients who were later shown to be affected by biliary atresia and cystic fibrosis the profile of bile acid metabolites was initially suggestive of a bile acid synthesis defect. Three adult patients suffered from cerebrotendinous xanthomatosis. Nineteen patients had peroxisomal disorders, and 10 patients had cholestatic hepatopathy of other cause. CONCLUSION: Screening for urinary cholanoids should be done in every infant with cholestatic hepatopathy as well as in children with progressive neurological disease to provide specific therapy.Dorothea Haas Hongying Gan-Schreier Claus-Dieter Langhans Tilman Rohrer Guido Engelmann Maura Heverin David W Russell Peter T Clayton Georg F Hoffmann Jürgen G Okun 2012World Journal of Gastroenterology2012,18,10:2
2Influence of micromixing on the free-radical polymerization in a discontinuous process显示文摘Engelmann U Schmidt-Naake G 1994Macromolecular Theory and Simulations1994,3,5:1
3Feasibility study and control values of transient elastography in healthy chil- dren 显示文摘Engelmann G Gebhardt C Wenning D 2012Eur J Pediatr2012,171,2:1
4Co deposition on Au(111) and Au(100) electrodes: an in situ STM study显示文摘KLEINERT M WAIBEL H F ENGELMANN G E 2001Electrochimica Acta2001,46,2021:1
5Differential behavioural effects of chronic infusion of CRH 1 and CRH 2 receptor antisense oligonucleotides into the rat brain显示文摘Liebsch G Landgraf R Engelmann M 1999J Psychiatr Res1999,33,2:1
6Nanoscale decoration of electrode surfaces with an STM显示文摘Kolb D M Engelmann G E Ziegler J C 2000Solid State Ionics2000,131,:1
7Combination of ultrasound and pneumatic lithotripsy 显示文摘Haupt G Engelmann U Menne A 2001J Urol2001,165,:1
8Effects of three resin monomers on the cellular glutathione concentration of cultured human gingival fibroblasts显示文摘Volk J Engelmann J Leyhausen G 2005Dent Mater2005,28,:1
9Activation and role of MAP kinase-dependent pathways in retinal pigment epithelial cells: ERK and RPE cell proliferation显示文摘Hecquet C Lefevre G Valtink M Engelmann K Mascarelli F 2002Invest Ophthalmol Vis Sci2002,43,:1
10Optimization of nonviral transfection: variables influencing liposome-mediated gene transfer in proliferating vs, quiescent cells in culture and in vivo using a porcine restenosis model显示文摘Pelisek J Engelmann M G Golda A 2002J Mol Med2002,80,11:1
11Automatic contact algorithm in DYNA3D for crashworthiness and impact problems显示文摘WHIRLEY R G ENGELMANN B E 1994Nuclear Engineering and Design1994,150,23:1
12The complete dechlorination of DDT by magnesium/palladium bimetallic particles 显示文摘Mark D Engelmann John G 2001Chemosphere2001,43,2:1
13Interdiffusion of CdS/CdTe thin films: modeling x-ray diffraction line profiles显示文摘McCandless B E Engelmann M G Birkmire R W 2001Journal of Applied Physics2001,89,2:1
14How can tumor cells escape in tercellular induction of apoptosiss ? 显示文摘Engelmann I Bauer G 2000Anticancer Res2000,20,4:1
15Vascular endothelial growth factor( VEGFI65 ) and its influence on angiogenesis versus arteriogenesis in different vascular beds 显示文摘Nikol S Pelisek J Engelmann M G 2002J Endovasc Ther2002,9,6:1
16Endophthalmitis after cataract surgery:predisposing factors,infectious agents and therapy显示文摘Zell K Engelmann K Bialasiewicz AA Richard G 2000Ophthalmologe2000,97,4:1
17Effects of three resin monomers on the cellular glutathione concentration of cultured hu- man gingival broblasts显示文摘Volk J Engelmann J Leyhausen G 2006Dent Mater2006,22,6:1
18Coumarin necrosis in Klinefelter's syndrome 显示文摘Klemm G Engelmann C 1977Z Gesamte Inn Med1977,32,24:1
19The Anaerobic Biodegradability of Municipal Sludge and Fat, Oil, and Grease at Mesophilic Conditions显示文摘Kabouris John C Tezel Ulas Pavlostathis Spyros G Engelmann Michael Todd Allen C Gillette Robert A 2008Water Environment Research2008,,3:1
20Identification and topology of variant sequences within individual repeat domains of the human epithelial tumor mucin MUC1 显示文摘Engelmann K Baldus S E Hanisch F G 2001J Biol Chem2001,276,27:1
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