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88篇 您的检索式：作者名="Engelmann F"

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	题名	作者	年代	出处	被引量
1	Differential diagnosis in patients with suspected bile acid synthesis defects显示文摘AIM: To investigate the clinical presentations associated with bile acid synthesis defects and to describe identification of individual disorders and diagnostic pitfalls. METHODS: We describe semiquantitative determination of 16 urinary bile acid metabolites by electrospray ionization-tandem mass spectrometry. Sample preparation was performed by solid-phase extraction. The total analysis time was 2 min per sample. We determined bile acid metabolites in 363 patients with suspected defects in bile acid metabolism. RESULTS: Abnormal bile acid metabolites were found in 36 patients. Two patients had bile acid synthesis defects but presented with atypical presentations. In 2 other patients who were later shown to be affected by biliary atresia and cystic fibrosis the profile of bile acid metabolites was initially suggestive of a bile acid synthesis defect. Three adult patients suffered from cerebrotendinous xanthomatosis. Nineteen patients had peroxisomal disorders, and 10 patients had cholestatic hepatopathy of other cause. CONCLUSION: Screening for urinary cholanoids should be done in every infant with cholestatic hepatopathy as well as in children with progressive neurological disease to provide specific therapy.	Dorothea Haas Hongying Gan-Schreier Claus-Dieter Langhans Tilman Rohrer Guido Engelmann Maura Heverin David W Russell Peter T Clayton Georg F Hoffmann Jürgen G Okun	2012	World Journal of Gastroenterology2012，18，10：	2
2	Development of cryopreservation for oil palm somatic embryos using an improved process显示文摘	Dumet D Engelmann F Chabrillange N and Duval Y	1993	Ol e agineux1993，48，：	1
3	Effect of various sugars and polyols on the tolerance to desiccation and freezing of oil palm polyembryonic cultures显示文摘	Dumet D Engelmann F Chabrillange N Dussert S Duval Y	1994	Seed Science P esearch1994，4，：	1
4	Plant cryopreservation : progress and prospects显示文摘	Engelmann F	2004	In Vitro Cellular Develop Biol Plant2004，40，5：	1
5	Co deposition on Au(111) and Au(100) electrodes: an in situ STM study显示文摘	KLEINERT M WAIBEL H F ENGELMANN G E	2001	Electrochimica Acta2001，46，2021：	1
6	Plant cryopreservation:Progress and prospects显示文摘	Engelmann F		0，，：	1
7	Cryopreservation of citrus apices using the encapsulation-dehydration technique显示文摘	Gonzalez-Arena M T Engelmann F Urra C	1998	Cryo-Letters1998，19，3：	1
8	Cryopreservation of apple shoot tips:importance of cryopreservation technique and of conditioning of donor plants显示文摘	Wu Y Engelmann F Zhao Y Zhou M Chen S	1999	CryoLetters1999，20，2：	1
9	Dual energy sub traction and temporal subtraction chest radiography 显示文摘	MacMahon H Li F Engelmann R	2008	Journal of Thoracic Imaging2008，23，：	1
10	Dual energy subtraction and temporal subtraction chest radiography 显示文摘	MacMahon H Li F Engelmann R	2008	J Thorac Imag- ing2008，23，2：	1
11	Separation of human X-spermatozoa by free-flow electrophoresis显示文摘	Engelmann U Krassnigg F	1988	Gamete Research1988，19，2：	1
12	Vitrification, encapsulation-vitrifi- cation and droplet-vitrification : a review 显示文摘	Sakai A Engelmann F	2007	CryoLetters2007，28，3：	1
13	Vitrification,encapsulation-vitrification and droplet-vitrification:A review显示文摘	Sakai A Engelmann F		0，，：	1
14	Activation and role of MAP kinase-dependent pathways in retinal pigment epithelial cells: ERK and RPE cell proliferation显示文摘	Hecquet C Lefevre G Valtink M Engelmann K Mascarelli F	2002	Invest Ophthalmol Vis Sci2002，43，：	1
15	Importance of desiccation for the cryopreservation of recalcitrant seed and vegetatively propagated species显示文摘	Engelmann F	1997	Plant Genet Res Newsletter1997，112，：	1
16	Plant eryopreservation: progress and prospects显示文摘	Engelmann F	2004	In Vitro Cellular & Developmental Biology of Plant2004，409，5：	1
17	Cryopreservation of plant germ- plasm using the encapsulation-dehydration technique: Review and case study on sugarcane 显示文摘	Ganzalez-Arnao M T Engelmann F	2006	Cryo Letters2006，27，3：	1
18	Soluble CD40 in the serum of healthy donors,patients with chronic renal failure,haemodialysis and chronic ambulatory peritoneal dialysis (CAPD) patients显示文摘	Schwabe R F Engelmann H Hess S	1999	Clin Exp Immunol1999，117，1：	1
19	Plant cryopreservation:progress and prospects显示文摘	Engelmann F	2004	In Vitro Cellular& Developmental Biology2004，40，：	1
20	Cryotherapy of shoot tips: a technique for pathogen eradication to produce healthy planting materials and prepare healthy plant genetic re- sources for cryopreservation 显示文摘	WANG Q C PANIS B ENGELMANN F	2009	Annals of Applied Biolo- gy2009，154，3：	1

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