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| 1 | Abernethy syndrome in Slovenian children: Five case reports and review of literature显示文摘BACKGROUND Abernethy syndrome is a congenital vascular anomaly in which the portal blood completely or partially bypasses the liver through a congenital portosystemic shunt.Although the number of recognized and reported cases is gradually increasing,Abernethy syndrome is still a rare disease entity,with an estimated prevalence between 1 per 30000 to 1 per 50000 cases.With this case series,we aimed to contribute to the growing knowledge of potential clinical presentations,course and complications of congenital portosystemic shunts(CPSS)in children.CASE SUMMARY Five children are presented in this case series:One female and four males,two with an intrahepatic CPSS and three with an extrahepatic CPSS.The first patient,who was diagnosed with an intrahepatic CPSS,presented with gastrointestinal bleeding,abdominal pain and hyperammonaemia at six years of age.He underwent a percutaneous embolization of his shunt and has remained asymptomatic ever since.The second patient presented with direct hyperbilirubinemia in the neonatal period and his intrahepatic CPSS later spontaneously regressed.The third patient had pulmonary hypertension and hyperammonaemia due to complete portal vein agenesis and underwent liver transplantation at five years of age.The fourth patient was diagnosed immediately after birth,when evaluated due to another congenital vascular anomaly,and the last patient presented as a teenager with recurrent bone fractures associated with severe osteoporosis.In addition,the last two patients are characterised by benign liver nodules;however,they are clinically stable on symptomatic therapy.CONCLUSION Abernethy syndrome is a rare anomaly with diverse clinical features,affecting almost all organ systems and presenting at any age. | Jerneja Pecek Petja Fister Matjaz Homan | 2020 | World Journal of Gastroenterology2020，26，37： | 6 |
| 2 | Variations in insti- tutional infrastructure, physician specialization and experi- ence and outcome in ovarian cancer: asystematic review 显示文摘 | DuBois A Rochon J P fisterer J | 2009 | Gynecol Oncol2009，112，2： | 1 |
| 3 | A small portable rainfall simulator for reproducible experi- ments on soil erosion显示文摘 | ISERLOH T FISTER W SEEGER M | 2012 | Soil - Tillage Research2012，124，4： | 1 |
| 4 | Gonadotropin releasing hormone type Ⅱ antagonists induce apoptotic cell death in human endometrial and ovarian cancer cells in vitro and in vivo显示文摘 | Fister S Gilnthert AR Emons G | 2007 | CancerRes2007，67，4： | 1 |
| 5 | Deposition system for the synthesis of modulated, ultrathin-film composites显示文摘 | FISTER L LI Xiao-mei MCCONNELL J | 1993 | Journal of Vacuum Science& Technology1993，11，6： | 1 |
| 6 | Benign familial neonatal convulsions caused by mutation inKCNQ3,exon 6 : a European case 显示文摘 | FISTER P ANETA SOLTIROVSKA-SALAMON A Debeljak M | 2013 | Eur J Paediatr Neurol2013，17，3： | 1 |
| 7 | Dividends and Directors : Do Outsiders Reduce Agency Costs? 显示文摘 | Belden Susan Fister Todd and Kanpp Bob | 2005 | Business & Society Review2005，，11： | 1 |
| 8 | Thyroid volume than ges during pregnancy and after delivery in an iodine-suffieient Republic of Slovenia 显示文摘 | Fister P Gaberseek S Zaletel K | 2009 | Eur J Obstet Gynecol Reprod Biol2009，145，1： | 1 |
| 9 | Synthesis of CuxMo6Se8 without Binary compounds as intermediates: a study using superlattices to kinetically control a solid-state reaction显示文摘 | FISTER L JOHNSON D C BROWN R | 1994 | Journal of American Chemical Society1994，116，： | 1 |
| 10 | Macrophage infected with cytopathic bovine viral diarrhea virus release a factor(s) capable of priming infected macrophages for activation-induced apoptoisis显示文摘 | Adler H P Fister H | 1997 | J Virol1997，71，： | 1 |
| 11 | The electrical conductivity of yttria-stabilized zirconia prepared by precipitation from inorganic aqueous solutions 显示文摘 | Brune A Lajavardi M Fister D | 1998 | Solid State Ionics1998，106，12： | 1 |
| 12 | Assessment of rpoB and 16S rRNA genes as targets for PCR-based identification of Pasteurella pneumotropica 显示文摘 | Dole VS Banu LA Fister RD | 2010 | Comp Med2010，60，6： | 1 |
| 13 | Gonadotropin- releasing hormone type Ⅱ antagonists induce apoptotic cell death in human endometrial and ovarian cancer cells in vitro and in vivo显示文摘 | Fister S Ganthert A R Emons G Grundker C | 2007 | Cancer Res2007，67，： | 1 |
| 14 | reading risk and reality: college students and reading for pleasure 显示文摘 | Fister J G A B | 2011 | CoUege&ResearchLibraries2011，72，5： | 1 |
| 15 | Counting single chromophore molecules for uhrasensitive analysis and separations on microchip devices显示文摘 | Fister J C Jacobson S C Davis L M | 1998 | Analytical Chemistry1998，70，3： | 1 |
| 16 | Gonadotropin-releasing hormone type II antagonists induce apoptotic cell death in human endometrial and ovarian cancer ceils in vitro and in vivo 显示文摘 | Fister S Gunthert AR Emons G | 2007 | Cancer Res2007，67，4： | 1 |
| 17 | For ERP Success, Create a Culture Change 显示文摘 | Sarah Fister Gale | 2002 | Workforce2002，81，9： | 1 |
| 18 | Changing Landscapes, Enduring Values: Making the Transition from Bibliographic In- struction to Information Literacy 显示文摘 | Hutchins E O Fister B MacPherson K | 2002 | Journal of Library Adminis- tration2002，36，12： | 1 |
| 19 | Thyroid volume changes during pregnancy and after delivery in an iodine sufficient Republic of Slovenia 显示文摘 | Fister P Gaberscek S Zaletel K | 2009 | Eur J Obstet Gynecol Reprod Biol2009，145，1： | 1 |
| 20 | Increase of doxorubicin- induced apoptosis after knock-down of gonadotropin-releasing hormone receptor expression in human endometrial, ovarian and breast cancer cells 显示文摘 | Fister S Schlotawa L Gunthert AR | 2008 | Gynecol Endocrinol2008，24，1： | 1 |
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