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| 1 | Increased expression of AQP 1 and AQP 5 in rat lungs ventilated with low tidal volume is time dependent 显示文摘 | Fabregat G Garc~a-de-la-Asunci6n J Sarri6 B | 2014 | PLoS One2014，9，14： | 1 |
| 2 | Advanced bioreductionof commercially important azo dyes:modeling and correlation withelectrochemical characteristics 显示文摘 | Mezohegyi G Fabregat A Font J | 2009 | Industrial & EngineeringChemistry Research2009，48，15： | 1 |
| 3 | Doubling exponent models for the analysis of porous film electrodes by impedance relaxation of TiO2 nanoporous in aqueous solution 显示文摘 | Bisquert J Garcia Belmonte G Fabregat Santiago F | 2000 | J Phys Chem B2000，104，10： | 1 |
| 4 | Symptomatic Val122del mutated hereditary transthyretin amyloidosis: Need for early diagnosis and prioritization for heart and liver transplantation显示文摘Background: Hereditary transthyretin(ATTRv) amyloidosis is an autosomal dominant disease linked to transthyretin gene mutations which cause instability of the transthyretin tetramer. After dissociation and misfolding they reassemble as insoluble fibrils(i.e. amyloid). Apart from the common Val30 Met mutation there is a very heterogeneous group of non-Val30 Met mutations. In some cases, the clinical picture is dominated by a rapidly evolving restrictive and hypertrophic cardiomyopathy. Methods: A case series of four liver recipients with the highly clinically relevant, rare and particularly aggressive Val122 del mutation is presented. Medical and surgical therapeutic options, waiting list policy for ATTRv-amyloidosis, including the need for heart transplantation, and status of heart-liver transplantation are discussed. Results: Three patients needed a staged(1 patient) or simultaneous(2 patients) heart-liver transplant due to rapidly progressing cardiac failure and/or neurologic disability. Domino liver transplantation was impossible in two due to fibrotic hepatic transformation caused by cardiomyopathy. After a follow-up ranging from 3.5 to 9.5 years, cardiac(allograft) function was maintained in all patients, but neuropathy progressed in three patients, one of whom died after 80 months. Conclusions: This is the first report in(liver) transplant literature about the rare Val122 del ATTRv mutation. Due to its aggressiveness, symptomatic patients should be prioritized on the liver and, in cases with cardiomyopathy, heart waiting lists in order to avoid the irreversible neurological and cardiac damage that leads to a rapid lethal outcome. | Adriano-Valerio Schettini Laura Llado JulieK Heimbach JoseGonzalez Costello Marie Tranäng Olivier Van Caenegem Richard C Daly Peter Van den Bergh Carlos Casasnovas Joan Fabregat John J Poterucha Maxime Foguenne Bo Göran Ericzon Jan Lerut | 2021 | Hepatobiliary & Pancreatic Diseases International2021，20，4： | 1 |
| 5 | Eval- uation of an environmentally friendly anticorrosive pigment for alkyd primer显示文摘 | MARTI M FABREGAT G AZAMBUJA D S | 2012 | Progress in Organic Coatings2012，73，4： | 1 |
| 6 | Spinal cord stimulation for the treatment of Buerger disease: a report on 3 cases显示文摘 | Fabregat G Villanueva VL Asensio JM | 2011 | Clin J Pain2011，27，9： | 1 |
| 7 | Increased expression of AQP 1and AQP 5 in rat lungs ventilated with low tidal volume is time dependent显示文摘 | Fabregat G García-de-la-Asunción J SarriáB | 2014 | PLoS One2014，9，11： | 1 |
| 8 | Postoperative pain management for patients who are long-term users of opioid 显示文摘 | Fabregat -Cid G Asensio -Samper JM Villanueva =P6rez V | 2011 | Rev Esp Anestesiol Reanim2011，58，1： | 1 |
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