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315篇 您的检索式：作者名="CLAYTON G"

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	题名	作者	年代	出处	被引量
1	Differential diagnosis in patients with suspected bile acid synthesis defects显示文摘AIM: To investigate the clinical presentations associated with bile acid synthesis defects and to describe identification of individual disorders and diagnostic pitfalls. METHODS: We describe semiquantitative determination of 16 urinary bile acid metabolites by electrospray ionization-tandem mass spectrometry. Sample preparation was performed by solid-phase extraction. The total analysis time was 2 min per sample. We determined bile acid metabolites in 363 patients with suspected defects in bile acid metabolism. RESULTS: Abnormal bile acid metabolites were found in 36 patients. Two patients had bile acid synthesis defects but presented with atypical presentations. In 2 other patients who were later shown to be affected by biliary atresia and cystic fibrosis the profile of bile acid metabolites was initially suggestive of a bile acid synthesis defect. Three adult patients suffered from cerebrotendinous xanthomatosis. Nineteen patients had peroxisomal disorders, and 10 patients had cholestatic hepatopathy of other cause. CONCLUSION: Screening for urinary cholanoids should be done in every infant with cholestatic hepatopathy as well as in children with progressive neurological disease to provide specific therapy.	Dorothea Haas Hongying Gan-Schreier Claus-Dieter Langhans Tilman Rohrer Guido Engelmann Maura Heverin David W Russell Peter T Clayton Georg F Hoffmann Jürgen G Okun	2012	World Journal of Gastroenterology2012，18，10：	2
2	The inorganic phosphates as polyelectrolytes显示文摘	Clayton F Callis John R Van Wazer Peter G Aryan	1954	Chemical Reviews1954，54，：	1
3	Gram-Schmidt orthogonalization显示文摘	Clayton D G	1971	Applied Statistics1971，20，3：	1
4	Stiffness ofgeomaterials at very small strains显示文摘	CLAYTON C R I HEYMANN G	2001	Geotechnique2001，51，3：	1
5	A statistical evaluation of animal and nutrional factors influencing concentrations of milk urea ni- trogen显示文摘	Broderick G A Clayton M C	1997	J Dairy Sci1997，80，：	1
6	Gram Sehmidt Orthogonallization显示文摘	Clayton D G	1971	Applied Statistics1971，20，3：	1
7	Molecular genetic aspects of human mitochondrial disorders 显示文摘	Larsson N G Clayton D A	1995	Annu Rev Genet1995，29，：	1
8	Comparison of a new colorimetric assay with the NCCLS broth microdilution method(M27-A) for antifungal drug MIC determination显示文摘	LI R K ELIE C M CLAYTON G E	2000	J Clin Microbiol2000，38，6：	1
9	Initiation and beyond:multiple functions of the human mitochondrial transcription machinery显示文摘	Bonawitz N D Clayton D A Shadel G S		0，，06：	1
10	Patty' s industrial hygiene and toxicology 显示文摘	CLAYTON G D	1981	Toxicology1981，3，：	1
11	An integrated analysis of the safety and tolerability of desvenlafaxine compared with placebo in the treatment of major depressive disorder显示文摘	Clayton A H Kornstein S G Rosas G	2009	CNS Spectr2009，14，4：	1
12	Investigations of the Uptake of Transuranic Radionuclides by Humic and Fulvic Acids Chemically Immobilized on Silica Gel and Their Competitive Release by Complexing Agents显示文摘	Bulman R A Szabo G Clayton R F	1997	Waste Management1997，17，4：	1
13	Soil microbial diversity and community structure under wheat as influenced by tillage and crop rotation显示文摘	LUPWAYI N Z RRICEW A CLAYTON G W	1998	Soil Biology and Biochemistry1998，30，13：	1
14	The development and applicationof the Jameson cell显示文摘	Clayton R Jameson G J Manlapig E V	1991	Minerals Engineering1991，4，711：	1
15	Group B streptococcus infection : risk and pre- vention显示文摘	Plumb J Clayton G	2013	Pract Midwife2013，16，7：	1
16	Mechanical and chemical properties of tantalum-implanted steels显示文摘	Hubler G K Singer IL Clayton C R	1985	Materials Science and Engineering1985，69，：	1
17	P2Y pu rinergic receptors regulate the growth of human melanomas显示文摘	White N Ryten M Clayton E Butler P Burnstock G	2005	Cancer Lett2005，224，：	1
18	A model for association in bivariate life tables and its application in epidemiological studies of familial tendency in chronic disease incidence 显示文摘	Clayton D G	1978	Biometrika1978，，65：	1
19	The effect of track and vehicle parameters on wheel/rail vertical dynamic forces显示文摘	JENKINS H STEPHENSON J CLAYTON G	1974	Railway Engineering Journal1974，，1：	1
20	Vitamin and mineral additives for meat quality 显示文摘	CLAYTON G	2001	Feed Intern2001，8，：	1

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